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當(dāng)前位置:首頁  >  產(chǎn)品中心  >  抗體/抗原  >  標(biāo)記一抗  >  bs-13681R-BioBiotin標(biāo)記的濕疹血小板減少伴免疫缺陷綜合征相關(guān)蛋白抗體

Biotin標(biāo)記的濕疹血小板減少伴免疫缺陷綜合征相關(guān)蛋白抗體

簡(jiǎn)要描述:The Wiskott-Aldrich syndrome (WAS) is a disorder that results from a monogenic defect that has been mapped to the short arm of the X chromosome. WAS is characterized by thrombocytopenia, eczema, defects in cell-mediated and humoral immunity and a propensity for lymphoproliferative disease. The gene that is mutated in the syndrome encodes a proline-rich protein of unknown function designated WAS protein (WASP). A clue to WASP function came from the observation that T cells from affected males

  • 產(chǎn)品型號(hào):bs-13681R-Bio
  • 廠商性質(zhì):生產(chǎn)廠家
  • 更新時(shí)間:2025-03-05
  • 訪  問  量: 145

詳細(xì)介紹

Human,Mouse(predicted: Rat,Cow,Rabbit)
WB
Shipped at 4℃. Store at -20°C for one year. Avoid repeated freeze/thaw cycles.

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